Vol. 3, Issue 2, Part C (2019)

Introduction: The idiopathic atrophodermia of Pasini and Pierini is a rare dermatosis described for the first time by Pasini in 1923 and Pierini in 1936. Its etiopathogenesis remains controversial. We report a new case.

Case report: A 32-year-old woman with no history of any particular medical condition who consults for non-pruritic brownish and atrophic skin lesions without associated inflammation and sclerosis of the trunk and limbs. Histological examination of a cutaneous fragment confirmed the diagnosis of atrophoderma by Pasini and Pierini. The patient was on topical corticosteroids combined with hydroxychloroquine 400 mg daily. The evolution was marked by a stabilization of lesions with a decline of one year.

Conclusion: this is a rare entity, easy diagnosis and variable therapeutic options that remain disappointing, however, because of the absence of involution of the lesions.