Vol. 4, Issue 3, Part D (2020)

Abstract: Supernumerary kidney is the rarest of all renal anomalies; fewer than 100 cases have been reported in the literature over the years. Supernumerary kidneys are most located on the left side of the abdomen. Different pathologic conditions are reported to affect supernumerary kidneys and they may be associated with malformations of the upper urinary tract and genital tract. Because of the scarcity of reported cases and atypical presentation, they frequently causes diagnostic difficulties. Incidence of Crossed fused kidney is 1:2000, second most common renal anomaly after Horseshoe kidney. Here we report a case of 20 year old male of unilateral supernumerary kidney on left side and crossed fused ectopia on right side. Supernumery kidney with crossed fused ectopia is the rarest renal anomaly.