Abstract: Background: Sinus pericranii (SP) is a rare vascular (venous) anomaly that connects the intracranial dural sinuses to the extracranial venous channels via emissary trans-osseous veins. It is a collection of non-muscular venous blood vessels that adhere tightly to the cranium and directly communicate with an intracranial venous sinus through diploic veins. About 200 cases have been reported worldwide, however numerous writers have tried to classify and treat this potentially fatal illness. Three unique cases of cranial abnormalities arrived. Different clinical presentations and initial patient care affected prognosis.
Methods: A retrospective study of three cases of congenital vascular SP was recorded in our department.
Results: All three cases were young, male, and had tumor-like masses in the left parieto-occipital venous abnormality improperly linking the intracranial dural sinuses with the epicranial veins. The tumours were entirely eliminated by surgery. By histopathology, vascular endothelium in the pathologic material supports congenital or spontaneous origin.
Conclusion: Paediatric sinus pericranii is uncommon and may be congenital or acquired. Incomplete sutural fusion or in-utero dural sinus thrombosis can induce congenital malformations. Usually involves the SSS and possibly TS, connected by diploic veins. All of our patients were congenital transverse sinus. Plain X-rays, CT, MR, and DSA can diagnose SP. Bony flaws, cortical thinning, and isolated erosions are shown on plain skull radiographs. Clinical examination and brain CT angiography with or without contrast are the most reliable diagnosis methods, and surgery is the best therapy. Resecting the extracranial venous package and ligating the emissary communication is crucial.
